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The invention discloses mannitol and/or proline containing compositions that are particularly useful for the treatment of premature ageing related symptoms in mammalian subjects suffering from genetic defects in DNA damage response and genome maintenance pathways. Humans suffering from Cockayne syndrome (CS), Xeroderma pigmentosum (XP), combined XPCS, trichothiodystrophy (TTD), COFS (cerebro-oculo-facio-skeletal syndro me), XFE disorder (Xpf-Ercc1 syndrome), Bloom Syndrome (BS), Werner Syndrome (WS), Ataxia telangiectasia (AT), Fanconi Anemia (FA), Hutchinson Guilford Progeria (HGP) may be treated with pharmaceutical compositions comprising mannitol and/or proline according to this invention.","lang":"en","source":"WIPO_FULLTEXT","data_format":"ORIGINAL"}],"fr":[{"text":"La présente invention concerne de nouveaux procédés et de nouveaux moyens destinés à la prévention et au traitement de symptômes et de maladies liés au vieillissement. L'invention concerne des compositions contenant du mannitol 5 et/ou de la proline qui sont particulièrement utiles pour le traitement de symptômes associés au vieillissement prématuré chez des sujets mammaliens souffrant d'anomalies génétiques au niveau des voies de réponse à une lésion de l'ADN et de maintien du génome. 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